TALE OF A MELTING FINGER: RARE CAUSE FOR PROGRESSIVE SHORTENING OF A DIGIT

Abstract

Gopi Surendra1, Sudha Kiran Das2, Sandeep Ramnal3, Kamal Kumar Sen4, Vikram B. Patil5

Vanishing bone disease aka Gorham- Stout disease is a rare entity of unknown aetiology, with no definite gender, race or sex predilection. It is characterised by destruction of osseous matrix and proliferation of vascular structures resulting in destruction and resorption of bone. It is usually monostotic, but can be polyostotic. Symptomatology is varied and depends on the site of involvement. We present a case and a short review of aetiopathogenesis, the radiological evolution of this rare condition and the therapeutic options available till date.

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