Pranati Mohanty1, Pallavi Bhuyan2, Asaranti Kar3, Pradeep Kumar Behera4, Chandra Sekhar Mohapatra5
BACKGROUND
Hemophagocytic Lymphohistiocytosis (HLH) is an uncommon, life-threatening and likely underdiagnosed disease of diverse aetiologies caused by a defective NK/T - cell cytotoxic pathway resulting in uncontrolled hypercytokinaemia leading to end organ damage carrying a high mortality rate. Here, we report HLH complicating SLE in a 42 years old female associated with disseminated histoplasmosis and accidentally detected as seropositive for HIV. This is extremely rare in the world literature.
