Blessy Mary Thomas1 , Elizabeth Joseph2 , Ajitha K.3
Classic renal angiomyolipoma (AML) is a benign mesenchymal tumour containing fat, smooth muscle cells and thick-walled blood vessels. However, renal epithelioid angiomyolipoma is considered as a potentially malignant neoplasm. It is a rare tumour constituting 4.6-4.8% of all resected AML. It is characterized by proliferation of predominantly epithelioid cells with approximately one third experiencing metastases. Epithelioid angiomyolipoma (EAML) is included in the family of perivascular epitheloid cell tumour (PECT)which is associated genetically with tuberous sclerosis complex.
