Narendranath Nagoti1, Amulya Chagalamarri2, Dwarakanath Nagoti3
Choledochal cysts are uncommon congenital anomalies of the biliary tree defined as abnormal, disproportionate, cystic dilatations of the biliary duct. (1) We report a 20 month old female child who presented with obstructive jaundice with recurrent episodes of cholangitis. She was diagnosed with a giant type IVA choledochal cyst with huge cystic dilatation of common bile duct (CBD) and multiple cystic dilatations of the intrahepatic biliary channels. The patient experienced complete recovery after the cyst was excised using LILLY technique and biliary reconstruction was done using Roux-en-Y hepatico jejunostomy at the level of the hilum. Here we discuss the clinical features and management of this giant type IVA choledochal cyst.