P. Ravi Kumar Reddy1, Uma Maheshwari S2, Akshay Hawal3, Diwakar Gaddi4
Anorectal malformation (ARM), one of the most common congenital defects, may present in a male child with a wide clinical spectrum of defects. These defects range from very minor and easily treatable ones with an excellent functional prognosis, to those that are complex, difficult to manage, often associated with other anomalies, and having a poor functional prognosis. Almost all patients present within first few days of life, delayed presentation being a rare entity. Single perineal orifice in a male child with delayed presentation is rarest encounter to the surgeon. The main concerns in correcting such anomalies are bowel and urinary control, and sexual function. With early diagnosis, management of associated anomalies and efficient meticulous surgical repair outcomes can be rewarding.