A. P. R. Naidu1, V. Murali Krishna2, L. Srijana3
Bardet Biedl syndrome includes presence of retinitis pimentosa along with obesity, polydactyl, hypogonadism, renal deformities,and learning disabilities. Orbital dystopia is any type of abnormal displacement of the entire orbital cones and their contents that can occur in three different dimensional planes. Situs describes the anatomic position of cardiac atria and visera. Situs solitus is normal anatomic position and situs inversus is the mirror image of the situs solitus. We report a case of a 13 year old male whom we diagnosed as a case of BBS with rare association with vertical orbital dystopia and situs inversus with dextrocardia.